간 및 신장의 종양과 신부전을 동반한 결절성 경화증 2예
Renal and Hepatic angiomyolipoma and Renal Failure in Two Cases of Tuberous Sclerosis
- Resource Type
- Article
- Authors
- 이동원 / Dong Won Lee; 허동 / Dong Hou; 김형옥 / Hyung Ok Kim; 김정원 / Chung Won Kim
- Source
- 대한피부과학회지 / Korean Journal of Dermatology. Feb 28, 1992 30(1):109
- Subject
- Angiomyolipoma
Tuberous sclerosis
- Language
- Korean
- ISSN
- 0494-4739
The abdominal manifestations of tuberous sclerosis are most frequently related to hamartomas of the kidneys which are readily detectable on CT scans because of their fat content. However, lipomas or angiomyolipomas of the liver are quite rare. Two patients with angiomyolipomas of the kidney had typical kin lesions of tuberous sclerosis. Orie had been on long-term dialysis for chronienal failure due to an angiomyolipomatous lesions and the other had undergone nephrectomy because of nonfunction kidney. Hepatic hamartomas were also seen in both atients. We should anticipate that such masses are not infrequent with uberous sclerosis. (Kor J Dermatol 1992; 30(1): 109-114)