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1 . Academic Journal
Ap4b1-knockout mouse model of hereditary spastic paraplegia type 47 displays motor dysfunction, aberrant brain morphology and ATG9A mislocalization.
저자
by
Scarrott, Joseph M.
;
Alves-Cruzeiro, João
;
Marchi, Paolo M.
;
Webster, Christopher P.
;
Zih-Liang Yang
, et al.
소스
Brain Communications; 2023, Vol. 5 Issue 1, p1-17, 17p
Open Access (OUP)
Scopus
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7 . Academic Journal
Loss of TMEM106B exacerbates C9ALS/FTD DPR pathology by disrupting autophagosome maturation.
저자
by
Bauer, Claudia S.
;
Webster, Christopher P.
;
Shaw, Allan C.
;
Kok, Jannigje R.
;
Castelli, Lydia M.
, et al.
소스
Frontiers in Cellular Neuroscience; 12/16/2022, Vol. 16, p01-18, 18p, 7 Graphs
Web of Science
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7 . Academic Journal
An interaction between synapsin and C9orf72 regulates excitatory synapses and is impaired in ALS/FTD.
저자
by
Bauer, Claudia S.
;
Cohen, Rebecca N.
;
Sironi, Francesca
;
Livesey, Matthew R.
;
Gillingwater, Thomas H.
, et al.
소스
Acta Neuropathologica
. Sep2022, Vol. 144 Issue 3, p437-464. 28p.
Web of Science
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7 . Academic Journal
C9ORF72-derived poly-GA DPRs undergo endocytic uptake in iAstrocytes and spread to motor neurons.
저자
by
Marchi, Paolo M.
;
Marrone, Lara
;
Brasseur, Laurent
;
Coens, Audrey
;
Webster, Christopher P.
, et al.
소스
Life Science Alliance; Sep2022, Vol. 5 Issue 9, p1-19, 19p
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7 . Academic Journal
SMN-deficient cells exhibit increased ribosomal DNA damage.
저자
by
Karyka, Evangelia
;
Ramirez, Nelly Berrueta
;
Webster, Christopher P.
;
Marchi, Paolo M.
;
Graves, Emily J.
, et al.
소스
Life Science Alliance; Aug2022, Vol. 5 Issue 8, p1-19, 19p
Web of Science
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7 . Academic Journal
C9orf72 plays a central role in Rab GTPase-dependent regulation of autophagy.
저자
by
Webster, Christopher P.
;
Smith, Emma F.
;
Grierson, Andrew J.
;
De Vos, Kurt J.
.
소스
Small GTPases
. 2018, Vol. 9 Issue 5, p399-408. 10p.
Scopus
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6 . Academic Journal
The hybrid AAVP tool gets an upgrade.
저자
by
Alves-Cruzeiro, João
;
Webster, Christopher P.
;
Azzouz, Mimoun
.
소스
Proceedings of the National Academy of Sciences of the United States of America
. 9/10/2019, Vol. 116 Issue 37, p18162-18164. 3p.
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5 . Academic Journal
Amyotrophic lateral sclerosis-associated mutant SOD1 inhibits anterograde axonal transport of mitochondria by reducing Miro1 levels.
저자
by
Moller, Annekathrin
;
Bauer, Claudia S.
;
Cohen, Rebecca N.
;
Webster, Christopher P.
;
De Vos, Kurt J.
.
소스
Human Molecular Genetics; Dec2017, Vol. 26 Issue 23, p4668-4679, 12p
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Full Text (OUP Near Archive)
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7 . Academic Journal
Protein Homeostasis in Amyotrophic Lateral Sclerosis: Therapeutic Opportunities?
저자
by
Webster, Christopher P.
;
Smith, Emma F.
;
Shaw, Pamela J.
;
De Vos, Kurt J.
.
소스
Frontiers in Molecular Neuroscience; 5/2/2017, Vol. 10, p1-22, 22p
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6 . Academic Journal
The C9orf72 protein interacts with Rab1a and the ULK1 complex to regulate initiation of autophagy
저자
by
Webster, Christopher P.
;
Smith, Emma F.
;
Bauer, Claudia S.
;
Moller, Annekathrin
;
Hautbergue, Guillaume M.
, et al.
소스
EMBO JOURNAL
; AUG 1 2016, 35 15, p1656-p1676, 21p.
Scopus
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