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1 . Academic Journal
Relationship Between Lung Volumes and Heterogeneity in the Response to Elexacaftor/Tezacaftor/Ivacaftor in Patients With Cystic Fibrosis and Advanced Lung Disease
저자
by
Gramegna, Andrea
;
Alicandro, Gianfranco
;
Premuda, Chiara
;
Lucca, Francesca
;
Pinali, Lucia
, et al.
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Chest
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7 . Academic Journal
In silico analysis and theratyping of an ultra-rare CFTR genotype (W57G/A234D) in primary human rectal and nasal epithelial cells
저자
by
Kleinfelder, Karina
;
Lotti, Virginia
;
Eramo, Adriana
;
Amato, Felice
;
Lo Cicero, Stefania
, et al.
소스
In
iScience
17 November 2023 26(11)
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7 . Academic Journal
Long-term clinical outcomes of elexacaftor/tezacaftor/ivacaftor therapy in adults with cystic fibrosis and advanced pulmonary disease
저자
by
Savi, Daniela
;
Lucca, Francesca
;
Tridello, Gloria
;
Meneghelli, Ilaria
;
Comello, Isabella
, et al.
소스
In
Respiratory Medicine
November-December 2023 219
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7 . Academic Journal
The effect of inhaled hypertonic saline on lung structure in children aged 3–6 years with cystic fibrosis (SHIP-CT): a multicentre, randomised, double-blind, controlled trial
저자
by
Andrinopoulou, Eleni-Rosalina
;
Anthony, Margaret M.
;
Au, Jacky
;
Belessis, Yvonne
;
Bonte, Merlijn
, et al.
소스
In
The Lancet Respiratory Medicine
July 2022 10(7):669-678
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7 . Academic Journal
Long-term safety and efficacy of tezacaftor–ivacaftor in individuals with cystic fibrosis aged 12 years or older who are homozygous or heterozygous for Phe508del CFTR (EXTEND): an open-label extension study
저자
by
Gibson, Ronald L., Jr.
;
Rowe, Steven M.
;
Lechtzin, Noah
;
Ahrens, Richard C.
;
McCoy, Karen S.
, et al.
소스
In
The Lancet Respiratory Medicine
July 2021 9(7):733-746
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7 . Academic Journal
Streptococcus pneumoniae oropharyngeal colonization in children and adolescents with cystic fibrosis
저자
by
Esposito, Susanna
;
Colombo, Carla
;
Tosco, Antonella
;
Montemitro, Enza
;
Volpi, Sonia
, et al.
소스
In
Journal of Cystic Fibrosis
May 2016 15(3):366-371
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7 . Academic Journal
The non‐invasive evaluation of liver involvement in patients with cystic fibrosis: A prospective study.
저자
by
Dajti, Elton
;
Ravaioli, Federico
;
Paiola, Giulia
;
Volpi, Sonia
;
Colecchia, Luigi
, et al.
소스
Liver International
. Nov2023, Vol. 43 Issue 11, p2492-2502. 11p.
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7 . Academic Journal
Bronchiectases at early chest computed tomography in children with cystic fibrosis are associated with increased risk of subsequent pulmonary exacerbations and chronic pseudomonas infection
저자
by
Bortoluzzi, Carla-Federica
;
Volpi, Sonia
;
D'Orazio, Ciro
;
Tiddens, Harm A.W.M.
;
Loeve, Martine
, et al.
소스
In
Journal of Cystic Fibrosis
September 2014 13(5):564-571
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7 . Academic Journal
Growth retardation and reduced growth hormone secretion in cystic fibrosis. Clinical observations from three CF centers
저자
by
Ciro, D'Orazio
;
Padoan, Rita
;
Blau, Hannah
;
Marostica, Anna
;
Fuoti, Maurizio
, et al.
소스
In
Journal of Cystic Fibrosis
August 2012
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7 . Academic Journal
THU-293 - The non-invasive evaluation of vascular liver disease in patients with cystic fibrosis: a prospective cross-sectional study
저자
by
Dajti, Elton
;
Ravaioli, Federico
;
Paiola, Giulia
;
Volpi, Sonia
;
Colecchia, Luigi
, et al.
소스
In
Journal of Hepatology
June 2023 78 Supplement 1:S974-S975
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