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1 . Academic Journal
Nonsense mutations accelerate lung disease and decrease survival of cystic fibrosis children
저자
by
Orenti, Annalisa
;
Pranke, Iwona
;
Faucon, Caroline
;
Varilh, Jessica
;
Hatton, Aurelie
, et al.
소스
In
Journal of Cystic Fibrosis
November 2023 22(6):1070-1079
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7 . Academic Journal
Keratin 8 is a scaffolding and regulatory protein of ERAD complexes.
저자
by
Pranke, Iwona Maria
;
Chevalier, Benoit
;
Premchandar, Aiswarya
;
Baatallah, Nesrine
;
Tomaszewski, Kamil F.
, et al.
소스
Cellular & Molecular Life Sciences
. Sep2022, Vol. 79 Issue 9, p1-19. 19p.
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7 . Academic Journal
New insights into structure and function of bis-phosphinic acid derivatives and implications for CFTR modulation.
저자
by
Bitam, Sara
;
Elbahnsi, Ahmad
;
Creste, Geordie
;
Pranke, Iwona
;
Chevalier, Benoit
, et al.
소스
Scientific Reports
. 3/25/2021, Vol. 11 Issue 1, p1-12. 12p.
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7 . Academic Journal
Characterization of two rat models of cystic fibrosis—KO and F508del CFTR—Generated by Crispr‐Cas9.
저자
by
Dreano, Elise
;
Bacchetta, Marc
;
Simonin, Juliette
;
Galmiche, Louise
;
Usal, Claire
, et al.
소스
Animal Models & Experimental Medicine; Dec2019, Vol. 2 Issue 4, p297-311, 15p
Open Access (Wiley)
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7 . Academic Journal
Author Correction: New insights into structure and function of bis-phosphinic acid derivatives and implications for CFTR modulation
저자
by
Bitam, Sara
;
Elbahnsi, Ahmad
;
Creste, Geordie
;
Pranke, Iwona
;
Chevalier, Benoit
, et al.
소스
Scientific Reports
. 11(1)
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7 . Academic Journal
Genetic deletion of keratin 8 corrects the altered bone formation and osteopenia in a mouse model of cystic fibrosis.
저자
by
Le Henaff, Carole
;
Da Cunha, Mélanie Faria
;
Hatton, Aurélie
;
Tondelier, Danielle
;
Marty, Caroline
, et al.
소스
Human Molecular Genetics; 4/1/2016, Vol. 25 Issue 7, p1281-1293, 13p
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7 . Academic Journal
Discovery of novel potent ΔF508-CFTR correctors that target the nucleotide binding domain
저자
by
Odolczyk, Norbert
;
Fritsch, Janine
;
Norez, Caroline
;
Servel, Nathalie
;
da Cunha, Melanie Faria
, et al.
소스
Embo Molecular Medicine
. Oct 01, 2013 5(10):1484-1501
Open Access (Wiley)
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7 . Periodical
A New Workflow for Proteomic Analysis of Urinary Exosomes and Assessment in Cystinuria Patients
저자
by
Bourderioux, Matthieu
;
Nguyen-Khoa, Thao
;
Chhuon, Cerina
;
Jeanson, Ludovic
;
Tondelier, Danielle
, et al.
소스
Journal of Proteome Research; January 2015, Vol. 14 Issue: 1 p567-577, 11p
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7 . Academic Journal
Effect of ouabain on CFTR gene expression in human Calu-3 cells.
저자
by
Baudouin-Legros, Maryvonne
;
Brouillard, Franck
;
Tondelier, Danielle
;
Hinzpeter, Alexandre
;
Edelman, Aleksander
.
소스
American Journal of Physiology: Cell Physiology
. Mar2003, Vol. 284 Issue 3, pC620. 7p. 6 Black and White Photographs, 1 Chart, 14 Graphs.
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7 . Academic Journal
Aspirin and some other nonsteroidal anti-inflammatory drugs inhibit cystic fibrosis transmembrane conductance regulator protein gene expression in T-84 cells.
저자
by
Tondelier, Danielle
;
Brouillard, Franck
;
Lipecka, Joanna
;
Labarthe, Regis
;
Bali, Moez
, et al.
소스
Mediators of Inflammation
. Aug99, Vol. 8 Issue 4/5, p219-227. 9p. 2 Charts.
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