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1 . Academic Journal
Homozygous missense mutation in UQCRC2 associated with severe encephalomyopathy, mitochondrial complex III assembly defect and activation of mitochondrial protein quality control
저자
by
Burska, Daniela
;
Stiburek, Lukas
;
Krizova, Jana
;
Vanisova, Marie
;
Martinek, Vaclav
, et al.
소스
In
BBA - Molecular Basis of Disease
1 August 2021 1867(8)
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7 . Academic Journal
The mammalian homologue of yeast Afg1 ATPase (lactation elevated 1) mediates degradation of nuclear-encoded complex IV subunits.
저자
by
Cesnekova, Jana
;
Rodinova, Marie
;
Hansikova, Hana
;
Houstek, Josef
;
Zeman, Jiri
, et al.
소스
Biochemical Journal
. 3/15/2016, Vol. 473 Issue 6, p797-804. 8p.
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7 . Academic Journal
Loss of Mitochondrial AAA Proteases AFG3L2 and YME1L Impairs Mitochondrial Structure and Respiratory Chain Biogenesis
저자
by
Cesnekova, Jana
;
Rodinova, Marie
;
Hansikova, Hana
;
Zeman, Jiri
;
Stiburek, Lukas
.
소스
INTERNATIONAL JOURNAL OF MOLECULAR SCIENCES
; DEC 2018, 19 12, p3930 13p.
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7 . Academic Journal
Assembly factors and ATP-dependent proteases in cytochrome c oxidase biogenesis
저자
by
Stiburek, Lukas
;
Zeman, Jiri
.
소스
BBA - Bioenergetics
. Jun2010, Vol. 1797 Issue 6/7, p1149-1158. 10p.
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4 . Academic Journal
Loss of function of Sco1 and its interaction with cytochrome c. oxidase.
저자
by
Stiburek, Lukas
;
Vesela, Katerina
;
Hansikova, Hana
;
Hulkova, Helena
;
Zeman, Jiri
.
소스
American Journal of Physiology: Cell Physiology
. May2009, Vol. 296 Issue 5, pC1218-C1226. 9p. 6 Graphs.
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7 . Academic Journal
The impact of mitochondrial tRNA mutations on the amount of ATP synthase differs in the brain compared to other tissues
저자
by
Fornuskova, Daniela
;
Brantova, Olga
;
Tesarova, Marketa
;
Stiburek, Lukas
;
Honzik, Tomas
, et al.
소스
BBA: Molecular Basis of Disease
. May2008, Vol. 1782 Issue 5, p317-325. 9p.
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7 . Academic Journal
Knockdown of Human Oxa1l Impairs the Biogenesis of F
1
F
o
-ATP Synthase and NADH:Ubiquinone Oxidoreductase
저자
by
Stiburek, Lukas
;
Fornuskova, Daniela
;
Wenchich, Laszlo
;
Pejznochova, Martina
;
Hansikova, Hana
, et al.
소스
Journal of Molecular Biology
. Nov2007, Vol. 374 Issue 2, p506-516. 11p.
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7 .
Impact of downregulation of gene expression of the peptidase subunit ClpP of the mitochondrial protease ClpXP on structure and function of mitochondria in human cells
저자
by
Kolařík, Daniel
;
Stibůrek, Lukáš
;
Pecina, Petr
.
소스
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5 .
Functional characterization of LACE1 APTase and mitochondrial AAA proteases YME1L and AFG3L2 in mitochondrial protein homeostasis
저자
by
Tesařová, Jana
;
Stibůrek, Lukáš
;
Kalous, Martin
;
Pecina, Petr
.
소스
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6 . Periodical
YME1L controls the accumulation of respiratory chain subunits and is required for apoptotic resistance, cristae morphogenesis, and cell proliferation
저자
by
Stiburek, Lukas
;
Cesnekova, Jana
;
Kostkova, Olga
;
Fornuskova, Daniela
;
Vinsova, Kamila
, et al.
소스
Molecular Biology of the Cell; March 2012, Vol. 23 Issue: 6 p1010-1023, 14p
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