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1 . Academic Journal
Comparative study on incorporation of three recombinant human α-galactosidase A drugs (agalsidases) into cultured fibroblasts and organs/tissues of Fabry mice
저자
by
Tsukimura, Takahiro
;
Shiga, Tomoko
;
Togawa, Tadayasu
;
Sakuraba, Hitoshi
.
소스
In
Molecular Genetics and Metabolism Reports
September 2024 40
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6 . Academic Journal
Does administration of hydroxychloroquine/amiodarone affect the efficacy of enzyme replacement therapy for Fabry mice?
저자
by
Tsukimura, Takahiro
;
Saito, Koki
;
Shiga, Tomoko
;
Ogawa, Yasuhiro
;
Sakuraba, Hitoshi
, et al.
소스
In
Molecular Genetics and Metabolism Reports
June 2024 39
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7 . Academic Journal
Comparative urinary globotriaosylceramide analysis by thin-layer chromatography-immunostaining and liquid chromatography-tandem mass spectrometry in patients with Fabry disease
저자
by
Shiga, Tomoko
;
Tsukimura, Takahiro
;
Namai, Yurie
;
Togawa, Tadayasu
;
Sakuraba, Hitoshi
.
소스
In
Molecular Genetics and Metabolism Reports
December 2021 29
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7 . Academic Journal
Effects of switching from agalsidase−α to agalsidase−β on biomarkers, renal and cardiac parameters, and disease severity in fabry disease forming neutralizing antidrug antibodies: a case report.
저자
by
Shima, Hisato
;
Tsukimura, Takahiro
;
Shiga, Tomoko
;
Togawa, Tadayasu
;
Sakuraba, Hitoshi
, et al.
소스
CEN Case Reports; Aug2024, Vol. 13 Issue 4, p290-296, 7p
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7 . Academic Journal
Novel Bernard-Soulier syndrome variants caused by compound heterozygous mutations (case I) or a cytoplasmic tail truncation (case II) of GPIbα
저자
by
Yamamoto, Naomasa
;
Akamatsu, Noriko
;
Sakuraba, Hitoshi
;
Matsuno, Kazuhiko
;
Hosoya, Ryota
, et al.
소스
In
Thrombosis Research
April 2013 131(4):e160-e167
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7 . Academic Journal
Binding parameters and thermodynamics of the interaction of imino sugars with a recombinant human acid α-glucosidase (alglucosidase alfa): Insight into the complex formation mechanism
저자
by
Yoshimizu, Michiru
;
Tajima, Youichi
;
Matsuzawa, Fumiko
;
Aikawa, Sei-ichi
;
Iwamoto, Kunihiko
, et al.
소스
In
Clinica Chimica Acta
May 2008 391(1-2):68-73
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7 . Academic Journal
Monitoring of anti-drug antibodies and disease-specific biomarkers in three patients from a Japanese Fabry family treated with enzyme replacement therapy.
저자
by
Kubota, Takao
;
Tsukimura, Takahiro
;
Shiga, Tomoko
;
Togawa, Tadayasu
;
Sakuraba, Hitoshi
.
소스
CEN Case Reports; May2023, Vol. 12 Issue 2, p171-175, 5p
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7 . Academic Journal
Cytochemical analysis of storage materials in cultured skin fibroblasts from patients with I-cell disease
저자
by
Kawashima, Ikuo
;
Ohsawa, Mai
;
Fukushige, Tomoko
;
Nagayama, Yoshihisa
;
Niida, Yo
, et al.
소스
In
Clinica Chimica Acta
2007 378(1):142-146
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7 . Academic Journal
Therapeutic evaluation of GM2 gangliosidoses by ELISA using anti-GM2 ganglioside antibodies
저자
by
Tsuji, Daisuke
;
Higashine, Yukari
;
Matsuoka, Kazuhiko
;
Sakuraba, Hitoshi
;
Itoh, Kohji
.
소스
In
Clinica Chimica Acta
2007 378(1):38-41
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7 . Academic Journal
Phospholipid storage in the myocardium of a unique Japanese case of idiopathic cardiomyopathy
저자
by
Kawashima, Ikuo
;
Takeuchi, Ichiro
;
Ohsawa, Mai
;
Kotani, Masaharu
;
Tajima, Youichi
, et al.
소스
In
Clinica Chimica Acta
2006 372(1):154-157
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