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1 . Academic Journal
Systematic multi‐level analysis of an organelle proteome reveals new peroxisomal functions
저자
by
Eden Yifrach
;
Duncan Holbrook‐Smith
;
Jérôme Bürgi
;
Alaa Othman
;
Miriam Eisenstein
, et al.
소스
Molecular Systems Biology, Vol 18, Iss 9, Pp n/a-n/a (2022)
Open Access (DOAJ)
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7 . Academic Journal
Impaired Bile Acid Homeostasis in Children with Severe Acute Malnutrition.
저자
by
Ling Zhang
;
Wieger Voskuijl
;
Marialena Mouzaki
;
Albert K Groen
;
Jennifer Alexander
, et al.
소스
PLoS ONE, Vol 11, Iss 5, p e0155143 (2016)
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7 . Academic Journal
C26:0-Carnitine Is a New Biomarker for X-Linked Adrenoleukodystrophy in Mice and Man.
저자
by
Malu-Clair van de Beek
;
Inge M E Dijkstra
;
Henk van Lenthe
;
Rob Ofman
;
Dalia Goldhaber-Pasillas
, et al.
소스
PLoS ONE, Vol 11, Iss 4, p e0154597 (2016)
Open Access (DOAJ)
Scopus
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7 . Academic Journal
Hydrogen sulfide donor NaHS reduces organ injury in a rat model of pneumococcal pneumosepsis, associated with improved bio-energetic status.
저자
by
Hamid Aslami
;
Wilco P Pulskens
;
Maria T Kuipers
;
Aafkeline P Bos
;
André B P van Kuilenburg
, et al.
소스
PLoS ONE, Vol 8, Iss 5, p e63497 (2013)
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7 . Academic Journal
Bezafibrate for X-linked adrenoleukodystrophy.
저자
by
Marc Engelen
;
Luc Tran
;
Rob Ofman
;
Josephine Brennecke
;
Ann B Moser
, et al.
소스
PLoS ONE, Vol 7, Iss 7, p e41013 (2012)
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7 . Academic Journal
Alkyl-glycerol rescues plasmalogen levels and pathology of ether-phospholipid deficient mice.
저자
by
Pedro Brites
;
Ana Sofia Ferreira
;
Tiago Ferreira da Silva
;
Vera F Sousa
;
Ana R Malheiro
, et al.
소스
PLoS ONE, Vol 6, Iss 12, p e28539 (2011)
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Scopus
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7 .
Systematic multi-level analysis of an organelle proteome reveals new peroxisomal functions
저자
by
Eden Yifrach
;
Duncan Holbrook-Smith
;
Jérôme Bürgi
;
Alaa Othman
;
Miriam Eisenstein
, et al.
소스
Open Access (OpenAIRE)
요약보기
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E-Mail
EndNote
RefWorks
7 .
Defective PEX gene products correlate with the protein import, biochemical abnormalities, and phenotypic heterogeneity in peroxisome biogenesis disorders
저자
by
Toshiro Tsukamoto
;
Guy T N Besley
;
Takashi Osumi
;
Naomi Kondo
;
Yasuyuki Suzuki
, et al.
소스
Journal of medical genetics, 36(10), 779-781. BMJ Publishing Group
Journal of Medical Genetics, 36, 779-781. BMJ Publishing Group
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7 .
IMPAIRED DEGRADATION OF LEUKOTRIENES IN PATIENTS WITH PEROXISOMAL DEFICIENCY DISORDERS
저자
by
Ertan Mayatepek
;
Gabriele Jedlitschky
;
Ruud B H Schutgens
;
Ronald J A Wanders
;
Dietrich Keppler
.
소스
Pediatric Research
. 32:627-627
Open Access (OpenAIRE)
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