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1 . Academic Journal
Central nervous system pathology in preclinical MPS IIIB dogs reveals progressive changes in clinically relevant brain regions
저자
by
Martin T. Egeland
;
Marta M. Tarczyluk-Wells
;
Melissa M. Asmar
;
Evan G. Adintori
;
Roger Lawrence
, et al.
소스
Scientific Reports, Vol 10, Iss 1, Pp 1-16 (2020)
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7 . Academic Journal
Natural history study of glycan accumulation in large animal models of GM2 gangliosidoses.
저자
by
Catlyn Cavender
;
Linley Mangini
;
Jeremy L Van Vleet
;
Carley Corado
;
Emma McCullagh
, et al.
소스
PLoS ONE, Vol 15, Iss 12, p e0243006 (2020)
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7 . Academic Journal
Characterization of glycan substrates accumulating in GM1 Gangliosidosis
저자
by
Roger Lawrence
;
Jeremy L. Van Vleet
;
Linley Mangini
;
Adam Harris
;
Nathan Martin
, et al.
소스
Molecular Genetics and Metabolism Reports, Vol 21, Iss , Pp - (2019)
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7 . Academic Journal
Clearance of Heparan Sulfate and Attenuation of CNS Pathology by Intracerebroventricular BMN 250 in Sanfilippo Type B Mice
저자
by
Mika Aoyagi-Scharber
;
Danielle Crippen-Harmon
;
Roger Lawrence
;
Jon Vincelette
;
Gouri Yogalingam
, et al.
소스
Molecular Therapy: Methods & Clinical Development, Vol 6, Iss C, Pp 43-53 (2017)
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7 . Academic Journal
Cellular internalization of alpha-synuclein aggregates by cell surface heparan sulfate depends on aggregate conformation and cell type
저자
by
Elisabet Ihse
;
Hodaka Yamakado
;
Xander M. van Wijk
;
Roger Lawrence
;
Jeffrey D. Esko
, et al.
소스
Scientific Reports, Vol 7, Iss 1, Pp 1-10 (2017)
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7 . Academic Journal
BMN 250, a fusion of lysosomal alpha-N-acetylglucosaminidase with IGF2, exhibits different patterns of cellular uptake into critical cell types of Sanfilippo syndrome B disease pathogenesis.
저자
by
Gouri Yogalingam
;
Amanda R Luu
;
Heather Prill
;
Melanie J Lo
;
Bryan Yip
, et al.
소스
PLoS ONE, Vol 14, Iss 1, p e0207836 (2019)
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7 . Academic Journal
The Effect of 1, 25 Dihydroxyvitamin D3 on Lymphocyte Transformation in Patients with Chronic Renal Failure
저자
by
Cetin ÖZENER
;
Emel AKOGLU
;
Roger LAWRENCE
;
Sukran ÖZGUN
;
Tevfik AKOGLU
, et al.
소스
Internal Medicine. 1995, 34(4):240
Open Access (JSTAGE)
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7 . Academic Journal
Ofloxacin-Induced Vasculitis
저자
by
Berrin Bagci CEYHAN
;
Murat SUNGUR
;
Rengin AHISKALI
;
Roger LAWRENCE
;
Turgay CELIKEL
.
소스
Internal Medicine. 1995, 34(9):872
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7 .
Biochemical evaluation of intracerebroventricular rhNAGLU-IGF2 enzyme replacement therapy in neonatal mice with Sanfilippo B syndrome
저자
by
Brett E. Crawford
;
Mark S. Sands
;
Ibrahim Elsharkawi
;
Steven Q. Le
;
Patricia I. Dickson
, et al.
소스
Mol Genet Metab
Open Access (OpenAIRE)
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7 .
Heat and Harmonics: Solutions to Concerns in Air-Cooled Medium-Voltage Adjustable-Speed Drives
저자
by
Roger Lawrence
;
Douglas Phares
;
Manish Verma
.
소스
IEEE Industry Applications Magazine
. 27:20-34
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