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1 . Academic Journal
Real-world treatment patterns and outcomes in patients with primary hemophagocytic lymphohistiocytosis treated with emapalumab
저자
by
Weinstein, Joanna
;
Hinson, Ashley P.
;
Allen, Carl E.
;
Eckstein, Olive S.
;
Gulati, Nitya
, et al.
소스
In
Blood Advances
14 May 2024 8(9):2248-2258
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7 . Academic Journal
Allogeneic hematopoietic cell transplantation is effective for p47phox chronic granulomatous disease: A Primary Immune Deficiency Treatment Consortium study
저자
by
Grunebaum, Eyal
;
Arnold, Danielle E.
;
Logan, Brent
;
Parikh, Suhag
;
Marsh, Rebecca A.
, et al.
소스
In
The Journal of Allergy and Clinical Immunology
May 2024 153(5):1423-1431
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7 . Academic Journal
Clinical and functional spectrum of RAC2-related immunodeficiency
저자
by
Donkó, Ágnes
;
Sharapova, Svetlana O.
;
Kabat, Juraj
;
Ganesan, Sundar
;
Hauck, Fabian H.
, et al.
소스
In
Blood
11 April 2024 143(15):1476-1487
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7 . Academic Journal
Relevance of lymphocyte proliferation to PHA in severe combined immunodeficiency (SCID) and T cell lymphopenia
저자
by
Abraham, Roshini S.
;
Basu, Amrita
;
Heimall, Jennifer R.
;
Dunn, Elizabeth
;
Yip, Alison
, et al.
소스
In
Clinical Immunology
April 2024 261
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7 . Academic Journal
Genotype, oxidase status, and preceding infection or autoinflammation do not affect allogeneic HCT outcomes for CGD
저자
by
Leiding, Jennifer W.
;
Arnold, Danielle E.
;
Parikh, Suhag
;
Logan, Brent
;
Marsh, Rebecca A.
, et al.
소스
In
Blood
14 December 2023 142(24):2105-2118
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7 . Academic Journal
Intestinal microbiome and metabolome signatures in patients with chronic granulomatous disease
저자
by
Chandrasekaran, Prabha
;
Han, Yu
;
Zerbe, Christa S.
;
Heller, Theo
;
DeRavin, Suk See
, et al.
소스
In
The Journal of Allergy and Clinical Immunology
December 2023 152(6):1619-1633
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7 . Academic Journal
Activated phosphoinositide 3-kinase δ syndrome: Update from the ESID Registry and comparison with other autoimmune-lymphoproliferative inborn errors of immunity
저자
by
Seidel, Markus G.
;
Seppänen, Mikko R.J.
;
Gennery, Andrew
;
Kanariou, Maria G.
;
Tantou, Sofia
, et al.
소스
In
The Journal of Allergy and Clinical Immunology
October 2023 152(4):984-996
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7 . Academic Journal
The diagnosis of severe combined immunodeficiency: Implementation of the PIDTC 2022 Definitions
저자
by
Dvorak, Christopher C.
;
Haddad, Elie
;
Heimall, Jennifer
;
Dunn, Elizabeth
;
Cowan, Morton J.
, et al.
소스
In
The Journal of Allergy and Clinical Immunology
February 2023 151(2):547-555
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7 . Academic Journal
NOX2 deficiency enhances priming and activation of the NLRP3 inflammasome
저자
by
Monjarret, Blandine
;
Shour, Sara
;
Benyoucef, Aissa
;
Heckel, Emilie
;
Marchitto, Lorie
, et al.
소스
In
The Journal of Allergy and Clinical Immunology
September 2023
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7 . Academic Journal
STAT3 gain-of-function mutations connect leukemia with autoimmune disease by pathological NKG2Dhi CD8+ T cell dysregulation and accumulation
저자
by
Masle-Farquhar, Etienne
;
Jackson, Katherine J.L.
;
Peters, Timothy J.
;
Al-Eryani, Ghamdan
;
Singh, Mandeep
, et al.
소스
In
Immunity
13 December 2022 55(12):2386-2404
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