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1 . Academic Journal
Reduced C9orf72 expression exacerbates polyGR toxicity in patient iPSC-derived motor neurons and a Type I protein arginine methyltransferase inhibitor reduces that toxicity
저자
by
Therese L. Dane
;
Anna L. Gill
;
Fernando G. Vieira
;
Kyle R. Denton
.
소스
Frontiers in Cellular Neuroscience, Vol 17 (2023)
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6 . Academic Journal
Impaired lipid metabolism in astrocytes underlies degeneration of cortical projection neurons in hereditary spastic paraplegia
저자
by
Yongchao Mou
;
Yi Dong
;
Zhenyu Chen
;
Kyle R. Denton
;
Michael O. Duff
, et al.
소스
Acta Neuropathologica Communications, Vol 8, Iss 1, Pp 1-20 (2020)
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7 . Academic Journal
Abnormal mitochondrial transport and morphology as early pathological changes in human models of spinal muscular atrophy
저자
by
Chong-Chong Xu
;
Kyle R. Denton
;
Zhi-Bo Wang
;
Xiaoqing Zhang
;
Xue-Jun Li
.
소스
Disease Models & Mechanisms, Vol 9, Iss 1, Pp 39-49 (2016)
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7 .
Impaired lipid metabolism in astrocytes underlies degeneration of cortical projection neurons in hereditary spastic paraplegia
저자
by
Xue-Jun Li
;
Michael O. Duff
;
Zhenyu Chen
;
Kyle R. Denton
;
Su-Chun Zhang
, et al.
소스
Acta Neuropathologica Communications
Acta Neuropathologica Communications, Vol 8, Iss 1, Pp 1-20 (2020)
Open Access (BioMed Central)
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7 .
Impaired mitochondrial dynamics underlie axonal defects in hereditary spastic paraplegias
저자
by
Kyle R. Denton
;
Dhruvi Shah
;
Jaerak Chang
;
Xue-Jun Li
;
Yongchao Mou
, et al.
소스
Human Molecular Genetics
. 27:2517-2530
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7 .
Recapitulating and Correcting Marfan Syndrome in a Cellular Model
저자
by
Wei Si
;
Bin Jiang
;
Siu-Pok Yee
;
Tiwanna M. Robinson
;
Zhenwu Zhang
, et al.
소스
International Journal of Biological Sciences
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7 .
Nuclear translocation of histone deacetylase 4 induces neuronal death in stroke
저자
by
Lin Liu
;
Sharon E. Benashski
;
Jun Li
;
Kyle R. Denton
;
Xue-Jun Li
, et al.
소스
Neurobiology of Disease, Vol 91, Iss, Pp 182-193 (2016)
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7 .
Pharmacologic rescue of axon growth defects in a human iPSC model of hereditary spastic paraplegia SPG3A
저자
by
Peng Peng Zhu
;
Tyler Mark Pierson
;
Craig Blackstone
;
Kyle R. Denton
;
Xue-Jun Li
.
소스
Human molecular genetics, vol 23, iss 21
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7 .
Loss of Spastin Function Results in Disease-Specific Axonal Defects in Human Pluripotent Stem Cell-Based Models of Hereditary Spastic Paraplegia
저자
by
Jeremy M. Grenier
;
Vladimir Rodionov
;
Ling Lei
;
Kyle R. Denton
;
Xue-Jun Li
, et al.
소스
Stem Cells
. 32:414-423
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7 .
Modeling Axonal Defects in Hereditary Spastic Paraplegia with Human Pluripotent Stem Cells
저자
by
Chongchong Xu
;
Kyle R. Denton
;
Harsh P. Shah
;
Xue-Jun Li
.
소스
Frontiers in biology
. 11(5)
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