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1 . Academic Journal
Mice with Ppt1Δex4 mutation replicate the INCL phenotype and show an inflammation-associated loss of interneurons
저자
by
Jalanko, Anu
;
Vesa, Jouni
;
Manninen, Tuula
;
von Schantz, Carina
;
Minye, Helena
, et al.
소스
In
Neurobiology of Disease
February 2005 18(1):226-241
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7 . Academic Journal
Dap12 and Trem2, molecules involved in innate immunity and neurodegeneration, are co-expressed in the CNS
저자
by
Kiialainen, Anna
;
Hovanes, Karine
;
Paloneva, Juha
;
Kopra, Outi
;
Peltonen, Leena
.
소스
In
Neurobiology of Disease
2005 18(2):314-322
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7 . Academic Journal
The mouse ortholog of the neuronal ceroid lipofuscinosis CLN5 gene encodes a soluble lysosomal glycoprotein expressed in the developing brain
저자
by
Holmberg, Ville
;
Jalanko, Anu
;
Isosomppi, Juha
;
Fabritius, Anna-Liisa
;
Peltonen, Leena
, et al.
소스
In
Neurobiology of Disease
2004 16(1):29-40
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7 . Academic Journal
Sialin expression in the CNS implicates extralysosomal function in neurons
저자
by
Aula, Nina
;
Kopra, Outi
;
Jalanko, Anu
;
Peltonen, Leena
.
소스
In
Neurobiology of Disease
2004 15(2):251-261
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6 . Academic Journal
ZNHIT3 is defective in PEHO syndrome, a severe encephalopathy with cerebellar granule neuron loss.
저자
by
Anttonen, Anna-Kaisa
;
Laari, Anni
;
Kousi, Maria
;
Yang, Yawei J.
;
Jääskeläinen, Tiina
, et al.
소스
Brain: A Journal of Neurology
. May2017, Vol. 140 Issue 5, p1267-1279. 13p.
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7 . Academic Journal
Abnormal microglial activation in the Cstb−/− mouse, a model for progressive myoclonus epilepsy, EPM1
저자
by
Okuneva, Olesya
;
Körber, Inken
;
Li, Zhilin
;
Tian, Li
;
Joensuu, Tarja
, et al.
소스
Glia
. Mar 01, 2015 63(3):400-411
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7 . Academic Journal
Abnormal microglial activation in the Cstb
−/−
mouse, a model for progressive myoclonus epilepsy, EPM1.
저자
by
Okuneva, Olesya
;
Körber, Inken
;
Li, Zhilin
;
Tian, Li
;
Joensuu, Tarja
, et al.
소스
Glia; Mar2015, Vol. 63 Issue 3, p400-411, 12p
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7 . Periodical
Impaired osteoclast homeostasis in the cystatin B-deficient mouse model of progressive myoclonus epilepsy
저자
by
Manninen, Otto
;
Puolakkainen, Tero
;
Lehto, Jemina
;
Harittu, Elina
;
Kallonen, Aki
, et al.
소스
Bone Reports; December 2015, Vol. 3 Issue: 1 p76-82, 7p
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7 . Academic Journal
Progressive Volume Loss and White Matter Degeneration in Cstb-Deficient Mice: A Diffusion Tensor and Longitudinal Volumetry MRI Study.
저자
by
Manninen, Otto
;
Laitinen, Teemu
;
Lehtimäki, Kimmo K.
;
Tegelberg, Saara
;
Lehesjoki, Anna-Elina
, et al.
소스
PLoS ONE
. Mar2014, Vol. 9 Issue 3, p1-7. 7p.
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7 . Academic Journal
Gene Expression Alterations in the Cerebellum and Granule Neurons of Cstb
−/−
Mouse Are Associated with Early Synaptic Changes and Inflammation.
저자
by
Joensuu, Tarja
;
Tegelberg, Saara
;
Reinmaa, Eva
;
Segerstråle, Mikael
;
Hakala, Paula
, et al.
소스
PLoS ONE
. Feb2014, Vol. 9 Issue 2, p1-12. 12p.
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