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1 . Academic Journal
Maintenance of cellular vitamin B6 levels and mitochondrial oxidative function depend on pyridoxal 5′-phosphate homeostasis protein
저자
by
Ciapaite, Jolita
;
van Roermund, Carlo W.T.
;
Bosma, Marjolein
;
Gerrits, Johan
;
Houten, Sander M.
, et al.
소스
In
Journal of Biological Chemistry
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7 . Academic Journal
Human peroxisomal NAD+/NADH homeostasis is regulated by two independent NAD(H) shuttle systems
저자
by
Chornyi, Serhii
;
Costa, Cláudio F.
;
IJlst, Lodewijk
;
Fransen, Marc
;
Wanders, Ronald J.A.
, et al.
소스
In
Free Radical Biology and Medicine
June 2023
Full Text (ScienceDirect)
Web of Science
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7 . Academic Journal
Barth syndrome cells display widespread remodeling of mitochondrial complexes without affecting metabolic flux distribution
저자
by
Chatzispyrou, Iliana A.
;
Guerrero-Castillo, Sergio
;
Held, Ntsiki M.
;
Ruiter, Jos P.N.
;
Denis, Simone W.
, et al.
소스
In
BBA - Molecular Basis of Disease
November 2018 1864(11):3650-3658
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7 . Academic Journal
Tracer‐based lipidomics enables the discovery of disease‐specific candidate biomarkers in mitochondrial β‐oxidation disorders.
저자
by
Schwantje, Marit
;
Mosegaard, Signe
;
Knottnerus, Suzan J. G.
;
van Klinken, Jan Bert
;
Wanders, Ronald J.
, et al.
소스
FASEB Journal
. 2/29/2024, Vol. 38 Issue 4, p1-17. 17p.
Web of Science
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7 . Academic Journal
Studying the topology of peroxisomal acyl-CoA synthetases using self-assembling split sfGFP.
저자
by
Chornyi, Serhii
;
Koster, Janet
;
IJlst, Lodewijk
;
Waterham, Hans R.
.
소스
Histochemistry & Cell Biology
. Feb2024, Vol. 161 Issue 2, p133-144. 12p.
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6 . Academic Journal
Altered interaction and distribution of glycosaminoglycans and growth factors in mucopolysaccharidosis type I bone disease
저자
by
Kingma, Sandra D.K.
;
Wagemans, Tom
;
IJlst, Lodewijk
;
Bronckers, Antonius L.J.J.
;
van Kuppevelt, Toin H.
, et al.
소스
In
Bone
July 2016 88:92-100
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7 . Academic Journal
Peroxisomal NAD(H) Homeostasis in the Yeast Debaryomyces hansenii Depends on Two Redox Shuttles and the NAD + Carrier, Pmp47.
저자
by
Turkolmez, Selva
;
Chornyi, Serhii
;
Alhajouj, Sondos
;
IJlst, Lodewijk
;
Waterham, Hans R.
, et al.
소스
Biomolecules (2218-273X)
. Sep2023, Vol. 13 Issue 9, p1294. 17p.
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7 . Academic Journal
Maintenance of cellular vitamin B
6
levels and mitochondrial oxidative function depend on pyridoxal 5'-phosphate homeostasis protein.
저자
by
Ciapaite, Jolita
;
van Roermund, Carlo W. T.
;
Bosma, Marjolein
;
Gerrits, Johan
;
Houten, Sander M.
, et al.
소스
Journal of Biological Chemistry
. Sep2023, Vol. 299 Issue 9, p1-15. 15p.
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7 . Academic Journal
Genetic, biochemical, and clinical spectrum of patients with mitochondrial trifunctional protein deficiency identified after the introduction of newborn screening in the Netherlands.
저자
by
Schwantje, Marit
;
Fuchs, Sabine A.
;
de Boer, Lonneke
;
Bosch, Annet M.
;
Cuppen, Inge
, et al.
소스
Journal of Inherited Metabolic Disease; Jul2022, Vol. 45 Issue 4, p804-818, 15p
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7 . Academic Journal
Synthesis and Intramitochondrial Levels of Valproyl-Coenzyme A Metabolites
저자
by
Silva, Margarida F.B.
;
Ruiter, Jos P.N.
;
IJlst, Lodewijk
;
Allers, Paul
;
ten Brink, Herman J.
, et al.
소스
In
Analytical Biochemistry
1 March 2001 290(1):60-67
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