Maurer, M, Magerl, M, Betschel, S, Aberer, W, Ansotegui, I J, Aygören-Pürsün, E, Banerji, A, Bara, N A, Boccon-Gibod, I, Bork, K, Bouillet, L, Boysen, H B, Brodszki, N, Busse, P J, Bygum, A, Caballero, T, Cancian, M, Castaldo, A J, Cohn, D M, Csuka, D, Farkas, H, Gompels, M, Gower, R, Grumach, A S, Guidos-Fogelbach, G, Hide, M, Kang, H R, Kaplan, A P, Katelaris, C H, Kiani-Alikhan, S, Lei, W T, Lockey, R F, Longhurst, H, Lumry, W, MacGinnitie, A, Malbran, A, Martinez Saguer, I, Matta Campos, J J, Nast, A, Nguyen, D, Nieto-Martinez, S A, Pawankar, R, Peter, J, Porebski, G, Prior, N, Reshef, A, Riedl, M, Ritchie, B, Sheikh, F R, Smith, W B, Spaeth, P J, Stobiecki, M, Toubi, E, Varga, L A, Weller, K, Zanichelli, A, Zhi, Y, Zuraw, B & Craig, T 2022, ' The international WAO/EAACI guideline for the management of hereditary angioedema – The 2021 revision and update ', World Allergy Organization Journal, vol. 15, no. 3, 100627 . https://doi.org/10.1016/j.waojou.2022.100627 World Allergy Organization journal, 15(3):100627. Lippincott Williams and Wilkins Maurer, Marcus; Magerl, Markus; Betschel, Stephen; Aberer, Werner; Ansotegui, Ignacio J; Aygören-Pürsün, Emel; Banerji, Aleena; Bara, Noémi-Anna; Boccon-Gibod, Isabelle; Bork, Konrad; Bouillet, Laurence; Boysen, Henrik Balle; Brodszki, Nicholas; Busse, Paula J; Bygum, Anette; Caballero, Teresa; Cancian, Mauro; Castaldo, Anthony J; Cohn, Danny M; Csuka, Dorottya; ... (2022). The international WAO/EAACI guideline for the management of hereditary angioedema-The 2021 revision and update. World Allergy Organization journal, 15(3), p. 100627. Wolters Kluwer Health Lippincott Williams & Wilkins 10.1016/j.waojou.2022.100627 The World Allergy Organization journal, vol 15, iss 3 Allergy: European Journal of Allergy and Clinical Immunology, 77(7), 1961-1990. Wiley-Blackwell