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1 . Academic Journal
Riociguat for the treatment of Phe508del homozygous adults with cystic fibrosis
저자
by
Derichs, Nico
;
Taylor-Cousar, Jennifer L.
;
Davies, Jane C.
;
Fajac, Isabelle
;
Tullis, Elizabeth
, et al.
소스
In
Journal of Cystic Fibrosis
November 2021 20(6):1018-1025
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7 . Academic Journal
Nasal potential difference in suspected cystic fibrosis patients with 5T polymorphism
저자
by
Aalbers, Bente L.
;
Yaakov, Yasmin
;
Derichs, Nico
;
Simmonds, Nicholas J.
;
De Wachter, Elke
, et al.
소스
In
Journal of Cystic Fibrosis
July 2020 19(4):627-631
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7 . Academic Journal
GLPG1837, a CFTR potentiator, in p.Gly551Asp (G551D)-CF patients: An open-label, single-arm, phase 2a study (SAPHIRA1)
저자
by
Davies, Jane C.
;
Van de Steen, Olivier
;
van Koningsbruggen-Rietschel, Silke
;
Drevinek, Pavel
;
Derichs, Nico
, et al.
소스
In
Journal of Cystic Fibrosis
September 2019 18(5):693-699
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7 . Academic Journal
Cystic Fibrosis Diagnostic Challenges over 4 Decades: Historical Perspectives and Lessons Learned
저자
by
Farrell, Philip M.
;
White, Terry B.
;
Derichs, Nico
;
Castellani, Carlo
;
Rosenstein, Beryl J.
.
소스
In
The Journal of Pediatrics
February 2017 181 Supplement:S16-S26
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7 . Academic Journal
Nasal potential difference measurements in diagnosis of cystic fibrosis: An international survey
저자
by
Naehrlich, Lutz
;
Ballmann, Manfred
;
Davies, Jane
;
Derichs, Nico
;
Gonska, Tanja
, et al.
소스
In
Journal of Cystic Fibrosis
January 2014 13(1):24-28
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7 . Academic Journal
Diagnosis of Cystic Fibrosis: Consensus Guidelines from the Cystic Fibrosis Foundation
저자
by
Farrell, Philip M.
;
White, Terry B.
;
Ren, Clement L.
;
Hempstead, Sarah E.
;
Accurso, Frank
, et al.
소스
In
The Journal of Pediatrics
February 2017 181 Supplement:S4-S15
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7 . Academic Journal
Diagnosis of Cystic Fibrosis in Nonscreened Populations
저자
by
Sosnay, Patrick R.
;
White, Terry B.
;
Farrell, Philip M.
;
Ren, Clement L.
;
Derichs, Nico
, et al.
소스
In
The Journal of Pediatrics
February 2017 181 Supplement:S52-S57
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7 . Academic Journal
The effect of CFTR modulation on the disease progression of cystic fibrosis in the era of precision medicine
저자
by
Stuart Elborn, J.
;
Davies, Jane
;
Bell, Scott
;
Derichs, Nico
.
소스
In
Journal of Cystic Fibrosis
March 2016 15(2):e20-e20
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6 . Conference
CFTR functional measurements in human models for diagnosis, prognosis and personalized therapy: Report on the pre-conference meeting to the 11th ECFS Basic Science Conference, Malta, 26–29 March 2014
저자
by
Beekman, Jeffrey M.
;
Sermet-Gaudelus, Isabelle
;
de Boeck, Kris
;
Gonska, Tanja
;
Derichs, Nico
, et al.
소스
In
Journal of Cystic Fibrosis
July 2014 13(4):363-372
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7 . Academic Journal
Local and Systemic Alterations of the L-Arginine/Nitric Oxide Pathway in Sputum, Blood, and Urine of Pediatric Cystic Fibrosis Patients and Effects of Antibiotic Treatment
저자
by
Hanusch, Beatrice
;
Brinkmann, Folke
;
Mayorandan, Sebene
;
Chobanyan-Juergens, Kristine
;
Wiemers, Anna
, et al.
소스
JOURNAL OF CLINICAL MEDICINE
; DEC 2020, 9 12, p3802 19p.
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