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1 . Academic Journal
Extending diagnostic practices in gyrate atrophy: Enzymatic characterization and the development of an in vitro pyridoxine responsiveness assay
저자
by
Balfoort, Berith M.
;
Pampalone, Gioena
;
Ruiter, Jos P.N.
;
Denis, Simone W.
;
Brands, Marion M.
, et al.
소스
In
Molecular Genetics and Metabolism
September-October 2024 143(1-2)
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7 . Academic Journal
Barth syndrome cells display widespread remodeling of mitochondrial complexes without affecting metabolic flux distribution
저자
by
Chatzispyrou, Iliana A.
;
Guerrero-Castillo, Sergio
;
Held, Ntsiki M.
;
Ruiter, Jos P.N.
;
Denis, Simone W.
, et al.
소스
In
BBA - Molecular Basis of Disease
November 2018 1864(11):3650-3658
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7 . Academic Journal
Upregulation of the AMPK-FOXO1-PDK4 pathway is a primary mechanism of pyruvate dehydrogenase activity reduction in tafazzin-deficient cells.
저자
by
Liang, Zhuqing
;
Ralph-Epps, Tyler
;
Schmidtke, Michael W.
;
Lazcano, Pablo
;
Denis, Simone W.
, et al.
소스
Scientific Reports
. 5/20/2024, Vol. 14 Issue 1, p1-15. 15p.
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7 . Academic Journal
Tracer‐based lipidomics enables the discovery of disease‐specific candidate biomarkers in mitochondrial β‐oxidation disorders.
저자
by
Schwantje, Marit
;
Mosegaard, Signe
;
Knottnerus, Suzan J. G.
;
van Klinken, Jan Bert
;
Wanders, Ronald J.
, et al.
소스
FASEB Journal
. 2/29/2024, Vol. 38 Issue 4, p1-17. 17p.
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7 . Academic Journal
A conserved complex lipid signature marks human muscle aging and responds to short-term exercise
저자
by
Janssens, Georges E.
;
Molenaars, Marte
;
Herzog, Katharina
;
Grevendonk, Lotte
;
Remie, Carlijn M. E.
, et al.
소스
Nature Aging
. 4(5):681-693
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7 . Academic Journal
Author Correction: Upregulation of the AMPK-FOXO1-PDK4 pathway is a primary mechanism of pyruvate dehydrogenase activity reduction in tafazzin-deficient cells
저자
by
Liang, Zhuqing
;
Ralph-Epps, Tyler
;
Schmidtke, Michael W.
;
Lazcano, Pablo
;
Denis, Simone W.
, et al.
소스
Scientific Reports
. 14(1)
Web of Science
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7 . Academic Journal
Detection of nonsterol isoprenoids by HPLC–MS/MS
저자
by
Henneman, Linda
;
van Cruchten, Arno G.
;
Denis, Simone W.
;
Amolins, Michael W.
;
Placzek, Andrew T.
, et al.
소스
In
Analytical Biochemistry
2008 383(1):18-24
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7 . Academic Journal
Lower Metabolic Potential and Impaired Metabolic Flexibility in Human Lymph Node Stromal Cells from Patients with Rheumatoid Arthritis.
저자
by
de Jong, Tineke A.
;
Semmelink, Johanna F.
;
Denis, Simone W.
;
Bolt, Janne W.
;
Maas, Mario
, et al.
소스
Cells (2073-4409)
. Jan2023, Vol. 12 Issue 1, p1. 14p.
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7 . Academic Journal
Inhibition of the neuromuscular acetylcholine receptor with atracurium activates FOXO/DAF‐16‐induced longevity.
저자
by
McIntyre, Rebecca L.
;
Denis, Simone W.
;
Kamble, Rashmi
;
Molenaars, Marte
;
Petr, Michael
, et al.
소스
Aging Cell
. Aug2021, Vol. 20 Issue 8, p1-16. 16p.
Open Access (Wiley)
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7 . Academic Journal
Quantification of Myocardial Creatine and Triglyceride Content in the Human Heart: Precision and Accuracy of in vivo Proton Magnetic Resonance Spectroscopy.
저자
by
Bakermans, Adrianus J.
;
Boekholdt, S. Matthijs
;
Vries, Dylan K.
;
Reckman, Yolan J.
;
Farag, Emile S.
, et al.
소스
Journal of Magnetic Resonance Imaging; Aug2021, Vol. 54 Issue 2, p411-420, 10p
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