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1 . Academic Journal
Lipid dysmetabolism in ceruloplasmin‐deficient mice revealed both in vivo and ex vivo by MRI, MRS and NMR analyses
저자
by
Valeria Mannella
;
Linda Chaabane
;
Tamara Canu
;
Alan Zanardi
;
Sara Raia
, et al.
소스
FEBS Open Bio, Vol 14, Iss 2, Pp 258-275 (2024)
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7 . Academic Journal
New orphan disease therapies from the proteome of industrial plasma processing waste- a treatment for aceruloplasminemia
저자
by
Alan Zanardi
;
Ilaria Nardini
;
Sara Raia
;
Antonio Conti
;
Barbara Ferrini
, et al.
소스
Communications Biology, Vol 7, Iss 1, Pp 1-17 (2024)
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7 . Academic Journal
Huntingtin-mediated axonal transport requires arginine methylation by PRMT6
저자
by
Alice Migazzi
;
Chiara Scaramuzzino
;
Eric N. Anderson
;
Debasmita Tripathy
;
Ivó H. Hernández
, et al.
소스
Cell Reports, Vol 35, Iss 2, Pp 108980- (2021)
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7 . Academic Journal
Striatal infusion of cholesterol promotes dose‐dependent behavioral benefits and exerts disease‐modifying effects in Huntington's disease mice
저자
by
Giulia Birolini
;
Marta Valenza
;
Eleonora Di Paolo
;
Elena Vezzoli
;
Francesca Talpo
, et al.
소스
EMBO Molecular Medicine, Vol 12, Iss 10, Pp n/a-n/a (2020)
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7 . Academic Journal
Polyglutamine expansion affects huntingtin conformation in multiple Huntington’s disease models
저자
by
Manuel Daldin
;
Valentina Fodale
;
Cristina Cariulo
;
Lucia Azzollini
;
Margherita Verani
, et al.
소스
Scientific Reports, Vol 7, Iss 1, Pp 1-15 (2017)
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7 . Academic Journal
Phospho-S129 Alpha-Synuclein Is Present in Human Plasma but Not in Cerebrospinal Fluid as Determined by an Ultrasensitive Immunoassay
저자
by
Cristina Cariulo
;
Paola Martufi
;
Margherita Verani
;
Lucia Azzollini
;
Giordana Bruni
, et al.
소스
Frontiers in Neuroscience, Vol 13 (2019)
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7 . Academic Journal
Recombinant Adeno Associated Viral (AAV) vector type 9 delivery of Ex1-Q138-mutant huntingtin in the rat striatum as a short-time model for in vivo studies in drug discovery
저자
by
Ilaria Ceccarelli
;
Pasquale Fiengo
;
Rosaria Remelli
;
Vincenzo Miragliotta
;
Lara Rossini
, et al.
소스
Neurobiology of Disease, Vol 86, Iss , Pp 41-51 (2016)
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7 . Academic Journal
Increased expression of the oligopeptidase THOP1 is a neuroprotective response to Aβ toxicity
저자
by
Giuseppe Pollio
;
Jeroen J.M. Hoozemans
;
Claus A. Andersen
;
Renza Roncarati
;
Maria Cristina Rosi
, et al.
소스
Neurobiology of Disease, Vol 31, Iss 1, Pp 145-158 (2008)
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7 . Academic Journal
Inhibition of Wnt signaling, modulation of Tau phosphorylation and induction of neuronal cell death by DKK1
저자
by
Carla Scali
;
Filippo Caraci
;
Marco Gianfriddo
;
Enrica Diodato
;
Renza Roncarati
, et al.
소스
Neurobiology of Disease, Vol 24, Iss 2, Pp 254-265 (2006)
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7 . Academic Journal
Polyglutamine- and temperature-dependent conformational rigidity in mutant huntingtin revealed by immunoassays and circular dichroism spectroscopy.
저자
by
Valentina Fodale
;
Natalie C Kegulian
;
Margherita Verani
;
Cristina Cariulo
;
Lucia Azzollini
, et al.
소스
PLoS ONE, Vol 9, Iss 12, p e112262 (2014)
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