Dural sinus malformation presenting with proptosis: report and review of a rare entity
- Resource Type
- Original Paper
- Authors
- Rao, Tejus M. N.; Thakar, Sumit; Pandey, Paritosh; Aryan, Saritha
- Source
- Child's Nervous System. 40(8):2599-2602
- Subject
- Dural sinus malformation
Arterio-venous shunt
Proptosis
- Language
- English
- ISSN
- 0256-7040
1433-0350
Dural sinus malformation (DSM) is a rare vascular malformation characterized by the dilatation of a dural venous sinus with or without an anomalous jugular bulb. Its presentation with venous-reflux-related secondary proptosis is anecdotal, with only six such cases reported so far. We report a 17-month-old boy who presented with a progressive proptosis of the right eye secondary to a DSM of the transverse sinus and torcula. Following endovascular embolization of the arterio-venous fistula, complete thrombosis of the venous lake and improvement in proptosis was noted at 6-month follow-up. Prognosis of this rare malformation is variable and dependent on specific angio-architectural features.