Evans Syndrome: A case report
- Resource Type
- Authors
- M. Romeo; E. Pitrolo; Simona Santucci; Mariella Valenzise; F. Chiera; Gilberto Candela; S. Nigro; Giuseppina Zirilli; Domenico Corica; Federica Porcaro
- Source
- La Pediatria Medica e Chirurgica, Vol 36, Iss 4 (2014)
- Subject
- medicine.medical_specialty
Neutropenia
Evans syndrome
Adolescent
Anemia
lcsh:Surgery
Aftercare
Gastroenterology
Autoimmune thrombocytopenia
Antibodies, Antineutrophil Cytoplasmic
autoimmune hemolytic anemia, autoimmune thrombocytopenia, Evans syndrome
hemic and lymphatic diseases
Internal medicine
medicine
Humans
Direct antiglobulin test
autoimmune hemolytic anemia
biology
business.industry
lcsh:RJ1-570
Immunoglobulins, Intravenous
lcsh:Pediatrics
lcsh:RD1-811
medicine.disease
Thrombocytopenia
autoimmune thrombocytopenia
Coombs Test
Pediatrics, Perinatology and Child Health
Immunology
biology.protein
Female
Steroids
Surgery
Anemia, Hemolytic, Autoimmune
Autoimmune hemolytic anemia
Antibody
business
- Language
- ISSN
- 0391-5387
We describe a case of a 14-years old caucasian female affected by autoimmune hemolytic anemia and thrombocytopenia successfully treated with intravenous immunoglobulin and steroids. Nevertheless, neutropenia occurred during follow-up period. Positivity of direct antiglobulin test and sieric anti-neutrophil antibodies suggested the diagnosis of Evans syndrome trilineage.