Superior vena cava obstruction and pulmonary artery involvement as rare findings of immunoglobulin G4-related disease
- Resource Type
- Authors
- Mihan Pourabdollah; Zargham Hossein Ahmadi; Neda Behzadnia; Faezeh Sheybani-Afshar; Babak Sharif-Kashani
- Source
- J Cardiol Cases
- Subject
- medicine.medical_specialty
biology
business.industry
Case Report
Disease
030204 cardiovascular system & hematology
medicine.disease
Pulmonary hypertension
Right pulmonary artery
03 medical and health sciences
0302 clinical medicine
Superior vena cava
medicine.artery
Internal medicine
Immunoglobulin g4
Pulmonary artery
medicine
Cardiology
biology.protein
030212 general & internal medicine
Antibody
Cardiology and Cardiovascular Medicine
business
Organ system
- Language
- English
We describe a case of immunoglobulin G4-related lung disease presenting as chronic pulmonary hypertension with involvement of right pulmonary artery and superior vena cava. Immunoglobulin G4- related disease is a rare systemic sclerosing disease with autoimmune entity that causes fibrotic, often mass-like manifestations that variably affect different organ systems and can be mistaken with other disorders. Timely diagnosis requires awareness on the part of clinicians and pathologists as well as radiologists to the variable manifestations of this newly recognized disorder.