Patent ductus arteriosus (PDA) is a relatively common congenital heart disease in which the ductus arteriosus fails to close after birth. PDA’s primary complications include left cardiac insufficiency, pulmonary hypertension, and right heart volume overload. Detection and evaluation of pulmonary hypertension level is a routine clinical concern, as it benefits treatment of PDA. However, few cases PDA with chronic thromboembolic pulmonary hypertension (CTEPH) have been reported. This study presents a 66-year-old male patient with PDA and CTEPH detected using computed tomography angiography (CTA). The main CTA imaging features include a PDA 3 cm in diameter, right pulmonary embolism with partial thrombosis calcification, pulmonary artery dilatation and pulmonary hypertension, and right ventricular enlargement.