There have been many reports on basal ganglia calcification (BGC) on computed tomography (CT) in adults. If only a little has been known about BGC in childhood by CT examination.We investigated the cases with BGC by screening all the CT films obtained for last 6 years (1979 April-1985 March) in the pediatric unit of our hospital. CT scanning was performed with Somatom SD and DR-II appratus and sections were obtained at an angle of 15° to the orbitometal line.BGC was found in 13 out of total 1, 637 cases. Confirmed diagnosis of these cases was as follows; pseudohypoparathyroidism (4), idiopathic hypoparathyroidism (1), mitochondrial encephalomyopathy (1), Cockayne's syndrome (1), brain tumor cases craniophariyngioma (1) and ectopic pinealoma (1), con-genital nephrotic syndrome (1), and unknown cases (3).The average of ages was 7 years old. The male to female ratio was 1 to 2.5. The locations of calcification were classified into 3 types. Globus pallidus only 4 cases, globus pallidus and other areas 7 cases, and other than globus pallidus 2 cases.In Cockayne's syndrome and craniopharyngioma, BGC was demonstrated also by plain roentogenogram. There were 3 cases whose BGC was recognized only at the 2 nd CT examination. No extrapyramidal sign was elicited except for the hand tremor found in the patient with Cockayne's syndrome. Convulsion was present in 8 patients. Abnormality in EEG was found in 9 out of the 11 patients subjected to the EEG examination.