A rare case of bilateral cystic nephroma associated with embryonal rhabdomyosarcoma of the penile urethra
- Resource Type
- article
- Authors
- Jujju Jacob Kurian; Sudipta Sen; Reju Thomas Joseph; Mandeep Singh Bindra
- Source
- Journal of Indian Association of Pediatric Surgeons, Vol 20, Iss 2, Pp 82-83 (2015)
- Subject
- Bilateral cystic nephroma
Dicer-1 mutation
urethral embryonal rhabdomyosarcoma
Pediatrics
RJ1-570
Surgery
RD1-811
- Language
- English
- ISSN
- 0971-9261
1998-3891
Bilateral cystic nephroma is an extremely rare benign renal neoplasm. Here we present a case of bilateral cystic nephroma in a four month old boy who subsequently developed embryonal rhabdomyosarcoma of the urethra. Both tumors were successfully treated. To our knowledge this is the first reported case of this association which could be related to Dicer-1 mutation.