[Rosai -Dorfman disease: a two cases report]
- Resource Type
- Authors
- Hadhami, Ben Turkia; Manal, Ben Romdhane; Hatem, Azzouz; Amel, Ben Chehida; Mohamed Slim, Abdelmoula; Rim, Ben Abdelaziz; Neji, Tebib; Monia, Ben Messoud; Samia, Sahtout; Ines, Chelly; Moncef, Zitouni; Emna, Mnif; Marie Francoise, Ben Dridi
- Source
- La Tunisie medicale. 89(5)
- Subject
- Young Adult
Disease Progression
Humans
Histiocytosis, Sinus
Child
- Language
- French
- ISSN
- 0041-4131
Rosai-Dorfman disease (RDD) is a benign lymphoproliferatif disorder characterized by cervical lymphadenopathies with a consistent risk of airways' compression and esthetical prejudice. Extra nodal localizations are also described.To report two pediatric cases of RDD.the first case concerned a patient with a prolonged nodal involvement of RDD. Remission seems to be natural although it coincided with a sulfaméthoxazole- triméthoprime therapy. The second case illustrated an extranodal form of RDD localized in soft tissue and paranasal sinus with extension to nasal cavity which were corticodependant.RDD is usually a benign disorder. Particular localizations, lack of effective therapy and the high risk of recurrence are important issues in this rare affection.