Primary Epithelioid Angiomyolipoma of Adrenal Gland: Case Report and Literature Review
- Resource Type
- Authors
- Muhammet, Cicek; Huseyin Ozgur, Kazan; Ramazan Gokhan, Atis; Asif, Yildirim
- Source
- Prague Medical Report. 123:199-205
- Subject
- Leukemia, Myeloid, Acute
Adrenal Glands
Angiomyolipoma
Humans
Adrenalectomy
Female
General Medicine
Middle Aged
Hormones
- Language
- ISSN
- 2336-2936
1214-6994
Angiomyolipomas (AMLs) are mesenchymal tumours derived from perivascular epithelioid cells. Although AMLs are generally known as benign and extremely rare epithelioid variants of AML, they may be potentially aggressive. Here we present an adrenal epithelioid AML and the literature review. A 64-year-old female patient was diagnosed with a left adrenal mass detected incidentally on ultrasonography. Preoperative abdominal CT (computed tomography) showed a 95×68 mm heterogeneous contrast enhancement mass lesion in the left adrenal gland. The lesion was hormone inactive in the endocrinological evaluation, and left laparoscopic adrenalectomy was performed. The patient was discharged on the 2nd postoperative day. Pathology was reported as epithelioid subtype AML. The patient has no local recurrence or metastasis in the 18-month follow-up period and imaging. Adrenal epithelioid AML is an extremely rare and potentially aggressive variant. According to the literature, open or laparoscopic adrenalectomy seems to be suitable option for disease management.