Supratentorial Haemangioblastoma without Von Hippel-Lindau Disease - A Rare Case Report with Review of Literature.
- Resource Type
- Article
- Authors
- SHAIKH, SALMAN TEHRAN; DEOPUJARI, CHANDRASHEKHAR EKNATH
- Source
- Journal of Clinical & Diagnostic Research. Oct2017, Vol. 11 Issue 10, p7-9. 3p.
- Subject
- *HEMANGIOBLASTOMAS
*CENTRAL nervous system
CENTRAL nervous system tumors
- Language
- ISSN
- 0973-709X
Haemangioblastomas are slow-growing, benign and vascular neoplasms of the central nervous system. They are usually infratentorial, occurring either sporadically in approximately 67% of cases or as a manifestation of Von Hippel-Lindau (VHL) disease in approximately 33% of cases. They were first described by Von Hippel in 1895. Haemangioblastoma in the supratentorial compartment is an infrequent occurrence. Only 58 cases of supratentorial haemangioblastoma without Von Hippel-Lindau disease have been reported from 1902 to 2015. This case discusses a left basifrontal supratentorial haemangioblastoma occurring in a young female who presented with headache and blurring of vision without manifestations of VHL disease. Its benign nature and prognosis merited surgical excision as the treatment of choice. [ABSTRACT FROM AUTHOR]